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VOLUME 10 , ISSUE 1 ( January-April, 2021 ) > List of Articles


Primary Pulmonary Synovial Sarcoma: How to Expect the Unexpected?

Mayank Yadav, Sumit Pratap Singh, Mohd Azam Haseen, Braj Mohan Singh, Noor Ahmad Lari, Mohammed Haneef Beg

Keywords : Immunohistochemistry, primary pulmonary synovial sarcoma, space-occupying lesion of lung

Citation Information : Yadav M, Singh SP, Haseen MA, Singh BM, Lari NA, Beg MH. Primary Pulmonary Synovial Sarcoma: How to Expect the Unexpected?. Indian J Respir Care 2021; 10 (1):136-138.

DOI: 10.4103/ijrc.ijrc_49_20

License: CC BY-NC-SA 4.0

Published Online: 06-12-2022

Copyright Statement:  Copyright © 2021; Indian Journal of Respiratory Care.


Primary pulmonary synovial sarcoma (PPSS) is a rare and aggressive malignancy with a presentation similar to that of lung carcinoma. We present an 18-year-old male who presented with complaints of chest pain, cough, and hemoptysis. Physical examination and blood parameters were normal. Imaging studies revealed a large, well-defined, round homogeneous mass in the left lower lobe. His fine-needle aspiration cytology was suggestive of a round cell tumor. The patient was operated under general anesthesia through left posterolateral thoracotomy. The tumor was removed en masse and sent for histopathological examination. His histopathology and immunohistochemistry suggested PPSS of biphasic variety.

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