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VOLUME 12 , ISSUE 4 ( October-December, 2023 ) > List of Articles

CASE REPORT

Left-sided Poland Syndrome Presenting as Chronic Respiratory Symptoms without Hand Deformity: A Rare Case Report

Mohit Bhatia, Gowthami Balasubramanian, Vijay Kumar, Priya Rajvansh

Keywords : Case report, Chest wall deformity, Chronic respiratory symptoms, Poland syndrome

Citation Information : Bhatia M, Balasubramanian G, Kumar V, Rajvansh P. Left-sided Poland Syndrome Presenting as Chronic Respiratory Symptoms without Hand Deformity: A Rare Case Report. Indian J Respir Care 2023; 12 (4):352-354.

DOI: 10.5005/jp-journals-11010-1069

License: CC BY-NC-SA 4.0

Published Online: 18-01-2024

Copyright Statement:  Copyright © 2023; The Author(s).


Abstract

A 31-year-old male presented with chronic respiratory symptoms (recurrent cough with expectoration, chest pain, and breathlessness) for the last 3 years. On physical examination, there was a chest wall deformity showing depression in the left-sided anterior chest wall with the absence of nipple on the left side. Chest X-ray showed decreased translucency on the left side. Further computed tomography (CT) of the thorax revealed nonvisualization of the left pectoralis major and minor muscles, with volume loss of left upper lobe and hypoplastic left anterior second rib and mild hypoplasia of body and xiphoid process of sternum. Spirometry showed a restrictive pattern of disease. So, diagnosis of Poland syndrome of left hemithorax was made. Patient was treated symptomatically and referred to a plastic surgeon for correction.


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